Images in Pathology - Gonadoblastoma with Distinctly Unusual Pattern of Yolk Sac Tumour Overgrowth

A 16-year-old girl with primary amenorrhoea presented with a two month history of a lump and discomfort in lower abdomen. She had lack of breast development, clitoromegaly and a pelvic mass. Ultrasonography revealed a heterogenous pelvic mass with calcific foci. CT scan showed a 13 x 10 x 9.5 cm mixed density pelvic mass. Karyotypic studies demonstrated 46-XY pattern. Exploratory laparotomy revealed a hypoplastic uterus, a large left ovarian mass with an intact capsule and a right streak ovary. There were no peritoneal deposits and the liver and lymph nodes were not involved. Both ovaries were removed.