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Neurology India
Medknow Publications on behalf of the Neurological Society of India
ISSN: 0028-3886
EISSN: 0028-3886
Vol. 53, No. 1, 2005, pp. 102-104
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Bioline Code: ni05029
Full paper language: English
Document type: Research Article
Document available free of charge
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Neurology India, Vol. 53, No. 1, 2005, pp. 102-104
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Case Report - Hallervorden spatz disease: MR and pathological findings of a rare case
Sharma MC, Aggarwal N, Bihari M, Goyal V, Gaikwed S, Vaishya S, Sarkar Chitra
Abstract
We describe a child with pathologically proven Hallervorden Spatz disease. He presented with extrapyramidal symptoms and characteristic "eye-of-the-tiger" sign on magnetic resonance imaging. He was given the possible benefit if any of deep brain stimulation with no much improvement. Pathological examination of the brain showed iron deposition in bilateral globus pallidi, spongiform change and neuron axonal degeneration (spheroids).
Keywords
Hallervorden Spatz disease, movement disorder, pantothenate kinase 2 deficiency
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