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East and Central African Journal of Surgery
Association of Surgeons of East Africa and College of Surgeons of East Central and Southern Africa
ISSN: 1024-297X EISSN: 1024-297X
Vol. 18, No. 1, 2013, pp. 135-139
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Bioline Code: js13018
Full paper language: English
Document type: Case Report
Document available free of charge
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East and Central African Journal of Surgery, Vol. 18, No. 1, 2013, pp. 135-139
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Pleuropulmonary Blastoma: Case Report
Tadesse, A.; Kidane, Philipos; Nega, Birhanu & Schneider, Jakob
Abstract
Pleuropulmonary blastoma (PPB) is a rare and aggressive tumor that is emerging as a
distinct entity of early childhood disease. It is characterized by mesenchymal elements
(including undifferentiated blastoma and often cartilaginous, rhabdomyoblastic, or
fibroblastic differentiation) and epithelium-lined spaces. The tumor arises in the lung and
pleura and is regarded as a pulmonary dysontogenetic or embryonic neoplasm. It is the
pulmonary analog of other tumors of childhood including Wilms` tumor, Neuroblastoma,
Hepatoblastoma, Pancreatoblastoma and Retinoblastoma. Due to their protean
presentation it is often difficult to make a preoperative diagnosis. A high index of suspicion
therefore is needed. As a result these are diagnosed late, and these, along with other
factors, affect the eventual outcome. We report a case of Pleuropulmonary blastoma
diagnosed after the child was operated as a case of massive left hemothorax following blunt
trauma.
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© Copyright 2013 - East and Central African Journal of Surgery
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